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Product Name | Calreticulin 3 (CALR3) (AA 20-384) protein (His tag) |
Description | Calreticulin-3 belongs to the calreticulin family, members of which are calcium binding chaperones localized mainly in the endoplasmic reticulum. It can be divided into a N-terminal globular domain, a proline-rich P-domain forming an elongated arm-like structure and a C-terminal acidic domain. During spermatogenesis process, Calreticulin-3 may act as a lectin-independent chaperone for specific client proteins such as ADAM3. Defects in CALR3 are the cause of familial hypertrophic cardiomyopathy type 19 (CMH19), it is a hereditary heart disorder characterized by ventricular hypertrophy, which is usually asymmetric and often involves the interventricular septum. The symptoms include dyspnea, syncope, collapse, palpitations, and chest pain.Alternative Names: Calreticulin-3, calreticulin-2, calsperin, CALR3, CRT2 |
Size | 1 mg |
Concentration | n/a |
Applications | n/a |
Other Names | AtCRT1b|T12M4.8|T12M4_8|calreticulin 1b|CMH19|CRT2|CT93|1700031L01Rik|6330586I20Rik|Crt2|cspn|A. thaliana calreticulin 3|AtCRT3|CALRETICULIN 3|EBS2|EMS-MUTAGENIZED BRI1 SUPPRESSOR 2|PRIORITY IN SWEET LIFE 1|PSL1|T27G7.13|T27G7_13|calreticulin 3 |
Gene, Accession, CAS # | Gene ID: 125972 |
Catalog # | ABIN1692463 |
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Order / More Info | Calreticulin 3 (CALR3) (AA 20-384) protein (His tag) from ANTIBODIES-ONLINE GmbH |
Product Specific References | n/a |
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