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| Antigenic Specificity | Solute Carrier Family 25 (Mitochondrial Carrier, Ornithine Transporter) Member 15 (SLC25A15) (N-Term) |
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| Clone | polyclonal |
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| Host Species | Rabbit |
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| Reactive Species | human |
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| Isotype | n/a |
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| Format | serum |
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| Size | 100 µL |
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| Concentration | n/a |
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| Applications | Immunohistochemistry (IHC),Western Blotting (WB) |
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| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
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| Description | Function: Ornithine transport across inner mitochondrial membrane, from the cytoplasm to the matrix. Defects in SLC25A15 are the cause of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome (HHH syndrome). It is an autosomal recessive disorder resulting in various neurologic symptoms, including mental retardation, spastic paraparesis with pyramidal signs, cerebellar ataxia, and episodic disturbance of consciousness or coma caused by hyperammonemia. It causes a functional impairment of the urea cycle.Subcellular location: Mitochondrion inner membrane, Multi-pass membrane protein Also known as: Mitochondrial ornithine transporter 1, Solute carrier family 25 member 15, ORNT1, SP1855. |
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| Immunogen | A synthetic peptide from n-terminal region of human SLC25A15 conjugated to blue carrier protein was used as the antigen. |
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| Other Names | Ab1-114|Ornt1|D630044L02Rik|D13S327|HHH|ORC1|ORNT1 |
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| Gene, Accession # | Gene ID: 10166 |
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| Catalog # | ABIN571492 |
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| Price | |
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| Order / More Info | Solute Carrier Family 25 (Mitochondrial Carrier, Ornithine Transporter) Member 15 (SLC25A15) (N-Term) Antibody from ANTIBODIES-ONLINE GmbH |
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| Product Specific References | n/a |
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