| 产品详情 |
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| Antigenic Specificity | BCKDHB |
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| Clone | polyclonal |
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| Host Species | Rabbit |
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| Reactive Species | human |
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| Isotype | n/a |
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| Format | peptide affinity purified |
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| Size | 80 µl, 400 µl |
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| Concentration | n/a |
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| Applications | WB, IHC, IF/ICC, FCM. RUO |
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| Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
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| Description | Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. This BCKDHB antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB. |
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| Immunogen | Human BCKDHB. |
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| Other Names | BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta; mitochondrial; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain |
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| Gene, Accession # | BCKDHB, SwissProt: P21953 |
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| Catalog # | abx025837 |
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| Price | |
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| Order / More Info | BCKDHB Antibody from ABBEXA |
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| Product Specific References | n/a |
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